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KMID : 0882420140860060739
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Korean Journal of Medicine
2014 Volume.86 No. 6 p.739 ~ p.743
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Systemic Amyloid Protein a Amyloidosis Involving the Heart in a Patient with Rheumatoid Arthritis
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Hwang Ji-Won
Jeon Eun-Seok
Ha Jung-Min
Lee Woo-Joo
Kim Eun
Yoon Se-Hyo
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Abstract
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Amyloidosis can be identified by the deposition of amyloid fibrils in biopsy specimens from multiple organs, including the heart, kidney, skin, and bowel. Systemic amyloid protein A amyloidosis (AA amyloidosis) is commonly associated with chronic inflammatory diseases or chronic infectious conditions. Cardiac involvement in AA amyloidosis is found in < 1% of reported cases. Here, we report a case of cardiac AA amyloidosis confirmed by heart biopsy in a 54-year-old-female with a medical history of rheumatoid arthritis and stage 4 chronic kidney disease due to renal amyloidosis. She had suffered from progressive aggravation of dyspnea for 2 years. Infiltrative disease involving the heart was suspected by echocardiography, and the patient was diagnosed with AA amyloidosis involving the heart by cardiac biopsy. This is a rare case of cardiac involvement in a patient with systemic AA amyloidosis associated with rheumatoid arthritis.
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KEYWORD
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Systemic amyloid protein A amyloidosis (AA amyloidosis), Congestive heart failure, Rheumatic arthritis
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